A Case of Desmoplastic Small Round Cell Tumor.
- Author:
Young Bun CHO
1
;
Hyo Seop AHN
;
Hee Young SHIN
;
Hyoung Soo CHOI
;
Eun Sil PARK
;
Chong Jai KIM
Author Information
1. Department of Pediatrics, Seoul Adventist Hospital, Seoul, Korea. ybejhs@medigate.net
- Publication Type:Case Report
- Keywords:
Desmoplastic small round cell tumor;
CA125, Surgical removal;
Chemotherapy
- MeSH:
Abdominal Pain;
Adolescent;
Desmoplastic Small Round Cell Tumor*;
Drug Therapy;
Drug Therapy, Combination;
Female;
Humans;
Young Adult
- From:Korean Journal of Pediatric Hematology-Oncology
2004;11(1):62-67
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Desmoplastic small round cell tumor (DSRCT) is a distinct clinicopathologic entity that has only recently been described. This aggressive malignant small cell neoplasm tends to occur in adolescents and young adults, who may present with vague abdominal discomfort or distention. We report a case of DSRCT in a 13 year-old girl who presented with intermittent abdominal pain and bulky intra-abdominal mass, accompanied by an increased serum level of a tumor marker CA125. Clinical, pathological, immunohistochemical and radiologic features were compatible with DSRCT. She is under aggressive combination chemotherapy after surgical resection.
