The result of dental and oral health status maintenance of pediatric patient with Papillon-Lefevre syndrome
- VernacularTitle:Папиллон-Лефеврийн хам шинжтэй хүүхдийн шүд, амны хөндийн байдлыг хянасан дүн
- Author:
Delgertsetseg J
1
,
2
;
Namuunzul Yo
3
;
Oyuntugs R
4
;
Munkhdul A
5
Author Information
1. Department of dental Hygiene, School of Dentistry, MNUMS
2. Department of dental Hygiene, Central Dental Hospital, MNUMS
3. 5th grade student, Dentistry curriculum, School of Dentistry, MNUMS
4. Department of Oral and Maxillofacial radiology, Central Dental Hospital, MNUMS
5. Department of Oral and Maxillofacial Surgery, School of Dentistry, Ach Medical University
- Publication Type:Case Reports
- Keywords:
Child, edentulous, alveolar bone resorption, tongue ulcer, genetic disorder
- From:
Mongolian Journal of Health Sciences
2025;87(3):108-114
- CountryMongolia
- Language:Mongolian
-
Abstract:
Background:Papillon-Lefevre Syndrome (PLS) is a rare genetic disorder,
characterized by palmoplantar keratosis, aggressive periodontitis and premature
edentulous primary and permanent dentition at a very young age. Additional
symptoms and findings associated with PLS may include frequent pyogenic
skin infections, abnormalities of the nails, and excessive perspiration.
Case report:The patient, who visited in the Central dental hospital was 3.6
years old. Pediatric dentist confirmed the diagnosis “PLS and chronic traumatic
tongue ulcer” based on anamnesis and objective examination. Dental and
tongue ulcer treatment was done once a week for 2 months. The recall system
was carried out by 3 month intervals oral examination and 6 month intervals
radiographic examinations under team of pediatric dentist, pediatrician and
immunologist.
- Full text:2025052420115015839108-115.pdf
