Ischemic polypectomy for small bowel polyps in pediatric Peutz-Jeghers syndrome
- VernacularTitle:Peutz-Jeghers хам шинжтэй хүүхдийн нарийн гэдсэн дэх ургацагийг энтероскопийн аргаар эмчилсэн тохиолдол
- Author:
Ulzii D
1
;
Sarantuya G
2
,
3
;
Sainzaya B
3
;
Sarangerel U
3
;
Khishigt N
3
;
Byambajav Ts
2
,
3
;
Enkhjin B
1
;
Tsevelnorov Kh
3
Author Information
1. Department of Pediatrics, School of Medicine, MNUMS
2. Department of Gastroenterology, School of Medicine, MNUMS
3. Endoscopy center, Mongolia-Japan Hospital, MNUMS
- Publication Type:Case Reports
- Keywords:
small bowel polyp, ischemic polypectomy, intussusception, doubleballoon enteroscopy
- From:
Mongolian Journal of Health Sciences
2025;87(3):35-39
- CountryMongolia
- Language:Mongolian
-
Abstract:
Backround:Peutz–Jeghers (PJ) syndrome is a rare autosomal dominant disorder
characterized by a mucocutaneous pigmentationon on oral mucosa and
multiple hamartomatous polyps located in the digestive tract except esophagus.
PJ syndrome can be diagnosed in early childhood by a characteristic pigmentation
and family history of polyposis. However, it is often diagnosed first
as a polyp in the small intestine that causes obstruction and intussusception
and is often treated with a bowel resection. If diagnosed in young childhood,
an effective non-invasive method is to resect the polyps by tying off the blood
supply to the polyps, that is the method named ischemic polypectomy, before
they grow to the point of obstruction using a endoscopy. PJ syndrome is rare
in Mongolia, but in severe cases, small intestine polyps are treated only surgically.
Double-balloon-endoscopy (DBE) has been performed at the Mongolian-
Japanese Hospital since 2023, making it possible to diagnose and treat
the syndrome endoscopically. Our patient, a 15-year-old boy, had a mucocutaneous
pigmentation that had been previously undiagnosed and was first diagnosed
with intussusception at the age of 13. He had undergone 4 endoscopic
procedures for upper and lower gastrointestinal polyps at the National Center
for Maternal and Child Health successfully. In our hospital, we found endoscopically
multiple hamartomatous polyps of various sizes between 1-3 cm,
and a 3 mm diameter tumor that filled 3/4 of the intestinal lumen was treated
by ischemic polypectomy.
After the procedure, there were no early or late complications related to
the procedure. The child's condition improved, the main complaints subsided,
and he continues his daily life normally. However, follow-up DBE is required.
- Full text:202505232038214005335-39.pdf
