Application of reimplantation technique in treating Marfan syndrome and giant aortic root aneurysm during mid-pregnancy: A case report
- VernacularTitle:应用reimplantation技术治疗妊娠中期马方综合征患者合并主动脉巨大根部瘤一例
- Author:
NIU
1
;
Hong QIAN
1
;
Haibo SONG
2
;
Lei DU
2
;
Hai YU
2
;
Eryong ZHANG
1
;
Zhenghua XIAO
1
Author Information
1. Department of Cardiovascular Surgery, West China Hospital, Sichuan University, Chengdu, 610041, P. R. China
2. Department of Anesthesiology, West China Hospital, Sichuan University, Chengdu, 610041, P. R. China
- Publication Type:Journal Article
- Keywords:
Marfan syndrome;
pregnancy;
valve-sparing root replacement;
aortic aneurysm;
case report
- From:
Chinese Journal of Clinical Thoracic and Cardiovascular Surgery
2025;32(03):416-420
- CountryChina
- Language:Chinese
-
Abstract:
Pregnancy complicated by aortic root aneurysm in patients with Marfan syndrome is one of the main causes of termination of pregnancy or even death in pregnant women. A very small number of pregnant women require cardiac surgery to preserve pregnancy under extracorporeal circulation, and all surgeries use aortic root replacement. We reported a 30-year-old patient with severe aortic regurgitation combined with giant aortic root aneurysm and Marfan syndrome in mid-pregnancy. Valve-sparing root replacement using reimplantation technology was performed via a multidisciplinary cooperation model. This not only achieved the patient’s desire to continue pregnancy but also avoided the anticoagulation and bleeding complications brought by mechanical valve replacement, reduced pregnancy risks and improved long-term quality of life. Postoperative echocardiography showed a small amount of aortic valve regurgitation, aortic valve coaptation height of 0.6 cm, effective height of 1.1 cm, maximum aortic flow velocity of 1.4 m/s, mean transvalvular pressure gradient of 4.4 mm Hg, and satisfactory clinical results.
