CT and MRI manifestations of lipofibromatosis in children
10.13929/j.issn.1003-3289.2024.09.025
- VernacularTitle:儿童脂肪纤维瘤病CT及MRI表现
- Author:
Changjian LI
1
;
Xu LI
;
Kefei HU
;
Xiaoyu WANG
;
Jun HU
Author Information
1. 安徽省儿童医院影像科,安徽 合肥 230051
- Keywords:
child;
fibromatosis,aggressive;
tomography,X-ray computer;
magnetic resonance imaging
- From:
Chinese Journal of Medical Imaging Technology
2024;40(9):1395-1399
- CountryChina
- Language:Chinese
-
Abstract:
Objective To observe CT and MRI manifestations of lipofibromatosis(LPF)in children.Methods Data of 16 children with LPF confirmed by pathology were retrospectively analyzed,and CT and MRI manifestations of lesions were observed.Results Among 16 cases,lesions with clear boundary were found in 4 cases but with unclear boundary in 12 cases,shaped regularly in 6 cases but irregularly in 10 cases,with incomplete capsule in 2 cases but without capsule in 14 cases.Fat predominant type lesions were detected in 6 cases,mainly characterized by scattered fibrous bands in the center or cloud like soft tissue density/signal on one side of lesion,without obvious boundary.Fibrous dominant type lesions were noticed in 8 cases,mainly present as loose morphology,multiple fibrous bands extending to surrounding area,with scattered cystic fat density/signal within the lesion.Balanced type LPF lesion was observed in 2 cases,mainly manifestated as regular shape mixed density/signal lesion with clear boundary.Among 12 cases who underwent enhanced scanning,mild progressive enhancement in the non-fat area were observed in 7 cases,obvious peripheral enhancement but not obvious central enhancement was found in 2 case,obvious homogeneous enhancement was noticed in 1 case,while no obvious enhancement was found in 2 cases.No obvious calcification,cystic changes nor bone destruction was detected.Conclusion CT and MRI manifestations of LPF included subcutaneous fat containing density/signal,often composed mainly of adipocytes or fibrous components,with mild progressive enhancement or significant enhancement,without obvious capsule,calcification,cystic changes nor bone destruction.
