Echocardiography for preoperative diagnosis and surgical planning of Ebstein anomaly in children
10.13929/j.issn.1003-3289.2024.07.002
- VernacularTitle:超声心动图用于术前诊断儿童埃布斯坦畸形及选择术式
- Author:
Leisheng ZHAO
1
;
Yuqi ZHANG
;
Lijun CHEN
;
Zhifang ZHANG
Author Information
1. 上海交通大学医学院附属上海儿童医学中心心内科,上海 200127
- Keywords:
Ebstein anomaly;
tricuspid valve;
ultrasonography
- From:
Chinese Journal of Medical Imaging Technology
2024;40(7):964-967
- CountryChina
- Language:Chinese
-
Abstract:
Objective To explore the value of echocardiography for preoperative diagnosis and surgical planning of Ebstein anomaly(EA)in children.Methods Echocardiography data of 216 EA children were retrospectively analyzed.The mitral valve-tricuspid valve distance(MTD),the ratio of distance from the root of anterior mitral leaflets to cardiac apex and distance from the root of the tricuspid valve septal leaflets to cardiac apex(MTR)were measured,and Glasgow outcome scale extended(GOSE)scores were calculated.The accuracy of MTD and MTR for diagnosing EA in children were compared,and the value of GOSE for surgical planning of EA was analyzed.Results Among 216 cases,descending tricuspid valve septum was observed with echocardiography in 199 cases.The accuracy of MTD＞15 mm,MTR＞1.2 and MTR＞1.5 for diagnosing EA in children was 81.91％(163/199),95.98％(191/199)and 68.34％(136/199),respectively,being significantly different(x2=9.802-51.856,all P＜0.001).Among 178 cases who underwent surgical operations,biventricular repair was performed in 101 cases,among them 90 cases with GOSE score≤1.00 recovered well after operation,while adverse events occurred in 5 cases among 11 cases(5/11,45.45％)with GOSE score＞1.00.One-and-a-half ventricle repair was performed in 62 cases who covered well after operation,including 22 cases with GOSE score≤1.00 and 40 cases＞1.00.Single-ventricular repair was performed in 15 cases with GOSE score＞1.00,and the patients recovered well after operation.Conclusion Preoperative echocardiography measured MTR＞1.2 was relatively reliable for accurately diagnosing EA in children.GOSE score was helpful for surgical planning.
