Atypical Teratoid/Rhabdoid Tumor in Central Nervous System: Report of 2 Cases.
- Author:
Jae Myung KIM
1
;
Young Shin RA
;
Thad T GHIM
;
Shin Kwang KHANG
Author Information
1. Department of Neurological Surgery, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, Korea. ysra@amc.seoul.kr
- Publication Type:Case Report
- Keywords:
Atypical teratoid/rhabdoid tumor;
Surgery;
Child;
Chemotherapy
- MeSH:
Central Nervous System*;
Child;
Drug Therapy;
Humans;
Infant;
Neural Plate;
Neuroectodermal Tumors, Primitive;
Prognosis
- From:Journal of Korean Neurosurgical Society
2002;32(6):599-602
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We report two cases of atypical teratoid/rhabdoid tumor(AT/RT) in the central nervous system. Primary central nervous system AT/RT is an extremely rare malignant tumor affecting infants and young children. These tumors have been diagnosed previously as primitive neuroectodermal tumors(PNETs) because AT/RT contains fields indistinguishable from classic PNETs. Separation of these two tumor types is crucial because the prognosis for AT/RT is poor even when treatment includes surgery with or without radiation therapy and/or chemotherapy. Clinical, radiological and histopathological features of AT/RT are presented.
