Development of a Pulmonary Arteriovenous Fistula after a Modified Glenn Shunt in Tetralogy of Fallot and Its Resolution after Shunt Takedown in a 57-Year-Old Patient.
10.5090/kjtcs.2017.50.3.215
- Author:
Sang Yoon KIM
1
;
Eung Rae KIM
;
Ji Hyun BANG
;
Woong Han KIM
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Korea. woonghan@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Fontan procedure;
Hepatopulmonary syndrome;
Pulmonary arteriovenous fistula;
Tetralogy of Fallot;
Angiogenesis inhibitor
- MeSH:
Arteriovenous Fistula*;
Cyanosis;
Dyspnea;
Embolization, Therapeutic;
Fontan Procedure;
Hepatopulmonary Syndrome;
Humans;
Lung;
Middle Aged*;
Perfusion;
Pulmonary Artery;
Tetralogy of Fallot*
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2017;50(3):215-219
- CountryRepublic of Korea
- Language:English
-
Abstract:
Pulmonary arteriovenous fistula (PAVF) is a complication of the Glenn shunt. A 57-year-old tetralogy of Fallot (TOF) patient, who had undergone a Glenn shunt and TOF total correction, complained of dyspnea and cyanosis. PAVFs were present in the right lung, and right lung perfusion was nearly absent. After coil embolization, takedown of the Glenn shunt, and reconstruction of the right pulmonary artery, the patient's symptoms were relieved. Extrapulmonary radioisotope uptake caused by the PAVFs shown in lung perfusion scans decreased, and right lung perfusion increased gradually. Although the development and resolution of PAVFs after a Glenn shunt have been reported in the pediatric population, this may be the first report on this change in old age.
