A Case of Catecholaminergic Polymorphic Ventricular Tachycardia.
10.3349/ymj.2009.50.3.448
- Author:
Seung Yul LEE
1
;
Jin Bae KIM
;
Eui IM
;
Woo In YANG
;
Boyoung JOUNG
;
Moon Hyoung LEE
;
Sung Soon KIM
Author Information
1. Division of Cardiology, Yonsei Cardiovascular Center and Cardiovascular Research Institute, Yonsei Univercity College of Medicine, Seoul, Korea. mhlee@yuhs.ac
- Publication Type:Case Report ; Review
- Keywords:
Catecholamine;
ventricular tachycardia
- MeSH:
Catecholamines/*metabolism;
Child;
Electrocardiography;
Female;
Humans;
Tachycardia, Ventricular/*diagnosis/genetics/pathology
- From:Yonsei Medical Journal
2009;50(3):448-451
- CountryRepublic of Korea
- Language:English
-
Abstract:
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a familial cardiac arrhythmia that is related to RYR2 or CASQ2 gene mutation. It occurs in patients with structurally normal heart and causes exercise-emotion-triggered syncope and sudden cardiac death. We experienced a case of CPVT in an 11 year-old female patient who was admitted for sudden cardiovascular collapse. The initial electrocardiogram (ECG) on emergency department revealed ventricular fibrillation. After multiple defibrillations, sinus rhythm was restored. However, recurrent ventricular fibrillation occurred during insertion of nasogastric tube without sedation in coronary care unit. On ECG monitoring, bidirectional ventricular tachycardia occurred with sinus tachycardia and then degenerated into ventricular fibrillation. To our knowledge, there has been no previous case report of CPVT triggered by sinus tachycardia in Korea. Therefore, we report the case as well as a review of the literature.
