Initiation of Torsades de pointes by head-up tilt test in congenital long QT syndrome patient.
10.4070/kcj.2000.30.8.1040
- Author:
Ik Soo JEON
;
Tae Joon CHA
;
Kil Soo KIM
;
Dong Wan KIM
;
Kyu Jong KIM
;
Seong Man KIM
;
Seong Jae JOO
;
Jae Woo LEE
- Publication Type:Case Report
- MeSH:
Death, Sudden;
Female;
Ganglionectomy;
Humans;
Long QT Syndrome*;
Mexiletine;
Seizures;
Syncope;
Tachycardia, Ventricular;
Torsades de Pointes*;
Young Adult
- From:Korean Circulation Journal
2000;30(8):1040-1044
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Long QT syndrome is a cardiac disorder of repolarization which is characterized by elctrocardiographic abnormalities including prolonged QT interval, T-wave abnormalities and polymorphic ventricular tachycardia known as Torsades de Pointes. Its clinical manifestation are recurrent syncope, seizure, and sudden death. Recently,we experienced Torsades de Pointes(TdP) by head-up tilt test in 24 year-old female patient presenting recurrent syncope and long QT interval. Beta-blocker and left cervicothoracic sympathetic ganglionectomy were not effictive, then we tried mexiletine. After mexiletine medication, the QT interval was significantly shortened and there was no more syncope.
