Herlyn-Werner-Wunderlich syndrome: An unusual presentation with pyocolpos.
10.5468/ogs.2017.60.4.374
- Author:
Eun Jung JUNG
1
;
Moon Hyeong CHO
;
Da Hyun KIM
;
Jung Mi BYUN
;
Young Nam KIM
;
Dae Hoon JEONG
;
Moon Su SUNG
;
Ki Tae KIM
;
Kyung Bok LEE
Author Information
1. Department of Obstetrics and Gynecology, Inje University Busan Paik Hospital, Busan, Korea. 107526@paik.ac.kr
- Publication Type:Case Report
- Keywords:
Herlyn-Werner-Wunderlich syndrome;
Renal agenesis;
Urogenital anomalies;
Uterus didelphys
- MeSH:
Adolescent;
Cervix Uteri;
Coinfection;
Diagnosis;
Drainage;
Dysmenorrhea;
Female;
Gynecological Examination;
Humans;
Magnetic Resonance Imaging;
Pelvic Pain;
Puberty;
Suppuration;
Uterus;
Vagina;
Vaginal Discharge;
Young Adult
- From:Obstetrics & Gynecology Science
2017;60(4):374-377
- CountryRepublic of Korea
- Language:English
-
Abstract:
Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly of the urogenital tract, which is characterized by the triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It usually presents at puberty with pelvic pain, dysmenorrhea, and a vaginal or pelvic mass. Although rare, it may present with purulent vaginal discharge due to secondary infection of the obstructed hemivagina, making diagnosis difficult. A careful pelvic examination to identify the cervix and vagina is the key to the diagnosis of Müllerian duct anomalies and magnetic resonance imaging can provide additional useful information. The optimal treatment is full excision and marsupialization of the obstructing vaginal septum so that both uteri can drain through the patent vagina. The authors report a case of a 22-year-old female with an unusual presentation of Herlyn-Werner-Wunderlich syndrome complicated by pyocolpos, which was successfully managed by vaginal septum resection and drainage of pus.
