Budd-Chiari syndrome associated with diaphragmatic hernia: A case report.
- Author:
Jung Won YUN
1
;
Young Bum PARK
;
Hwi KONG
;
Sung Won JUNG
;
Tae Kwang LEE
;
Jae Min SONG
Author Information
1. Department of Internal Medicine, Armed Forces Capital Hospital, Sungnam, Korea. jwcare@medimail.co.kr
- Publication Type:Case Report
- Keywords:
Budd-Chiari syndrome;
Hernia;
Diaphragmatic
- MeSH:
Abdominal Cavity;
Budd-Chiari Syndrome*;
Diaphragm;
Hepatic Veins;
Hernia;
Hernia, Diaphragmatic*;
Humans;
Liver;
Membranes;
Rare Diseases;
Thrombosis;
Vena Cava, Inferior;
Young Adult
- From:Korean Journal of Medicine
2005;69(6):692-695
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Budd-Chiari syndrome (BCS) is a rare disease caused by the obstruction of the hepatic venous outflow or the inferior vena cava above the hepatic vein. It has been attributed to various etiologic factors. Including intrinsic vascular thrombosis, hepatic tumor invasion/compression, or associated with an idiopathic obstructing membrane. However, in most cases no definitive etiologic factors have been identified. Recently, we experienced a case of 21-year-old man who had Budd-Chiari syndrome associated with diaphragmatic hernia. Venous flow returned to normal on reintroduction of the liver into the abdominal cavity and closure of the defect in the diaphragm. To our knowledge, this is the rare report in our country. Here, we report this case with review of literatures.