Acute Polymyositis/systemic Lupus Erythematosus Overlap Syndrome with Severe Subcutaneous Edema and Interstitial Lung Disease.
- Author:
U Ram JIN
1
;
Kyu Sung KWACK
;
Kyung Joo PARK
;
Ji Eun KWON
;
Si Yeon KIM
;
Ki Chan KIM
;
Ga Yong BAN
;
Ju Yang JUNG
;
Chang Hee SUH
;
Hyoun Ah KIM
Author Information
- Publication Type:Case Report
- Keywords: Inflammatory myopathy; Overlap syndrome; Subcutaneous edema; Interstitial lung disease
- MeSH: Edema*; Female; Glucocorticoids; Humans; Immunoglobulins; Immunosuppressive Agents; Lung Diseases, Interstitial*; Middle Aged; Muscle Weakness; Muscles; Myositis
- From:Journal of Rheumatic Diseases 2014;21(1):25-29
- CountryRepublic of Korea
- Language:English
- Abstract: Inflammatory myopathy is characterized by symmetrical proximal muscle weakness, elevated muscle enzyme levels and favorable response to glucocorticoids therapy. Although periorbital edema is a common manifestation of inflammatory myopathy, generalized subcutaneous edema is very rare. We report here a case of a 47-year-old female patient with acute polymyositis/systemic lupus erythematosus overlap syndrome with generalized subcutaneous edema and interstitial lung disease. We aggressively treated the disease with high-dose glucocorticoids, intravenous immunoglobulin, and immunosuppressive agents.
