A Case of Sclerosing Encapsulating Peritonitis Presented with Systemic Lupus Erythematosus.
- Author:
Sang Chul BAE
1
;
Joo Hyun PARK
;
Han Eol CHANG
;
Joo Hyun LEE
;
You Sun KIM
;
Jong Chum NAH
;
Bo Young YOON
Author Information
- Publication Type:Case Report
- Keywords: Systemic lupus erythematosus; Sclerosing encapsulating peritonitis
- MeSH: Abdominal Pain; Biopsy; Diagnosis; Heart Failure; Hemorrhage; Humans; Immunoglobulins; Intestine, Small; Lupus Erythematosus, Systemic*; Malnutrition; Methylprednisolone; Peritoneal Dialysis; Peritoneal Fibrosis; Peritoneum; Peritonitis*; Prevalence; Young Adult
- From:Journal of Rheumatic Diseases 2014;21(1):30-34
- CountryRepublic of Korea
- Language:Korean
- Abstract: Sclerosing encapsulating peritonitis (SEP) is characterized by peritoneal fibrosis and adhesion of the peritoneum with the loops of the small intestine. Although the prevalence is low, most cases are caused by peritoneal dialysis, infection, medication, systemic lupus erythematosus (SLE), and intra-abdominal neoplasm. We describe a 22-year old man who was presented with abdominal pain and distension, which were attributed to SLE with peritonitis. He had no specific history of previous medical illness and peritoneal dialysis. He was treated with intravenous high dose methylprednisolone 1 g/day for 3 days, followed by intravenous methylprednisolone 1 mg/kg daily and immunoglobulin. However, his symptoms did not improve. Eventually, a laparoscopic biopsy was performed for an accurate diagnosis. The histopathologic findings were presented in accordance to the typical characteristics of SEP. In spite of medical treatment, he did not show an improvement of clinical symptoms and radiologic findings. As a result, he died from nutritional deficiency, upper gastrointestinal bleeding, and congestive heart failure.
