A Case of Dissection in Marfan Syndrome with Ascending Aortic Aneurysm.
10.12701/yujm.1989.6.1.179
- Author:
Bong Young YOON
;
Chang Heon YANG
;
Young Jo KIM
;
Bong Sup SHIM
;
Hyun Woo LEE
;
Han Young RYU
;
Tae Eun JUNG
;
Yee Tae PARK
;
Sung Sae HAN
- Publication Type:Case Report
- MeSH:
Aneurysm, Dissecting;
Aorta;
Aortic Aneurysm*;
Aortic Valve Insufficiency;
Cardiovascular System;
Connective Tissue Diseases;
Humans;
Marfan Syndrome*;
Mitral Valve Insufficiency;
Musculoskeletal System
- From:Yeungnam University Journal of Medicine
1989;6(1):179-184
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The Marfan syndrome is a generalized connective tissue disease involving eye, musculoskeletal system, cardiovascular system, and inherited autosomal dominant with various expression type. The cardiovascular complications such as aortic aneurysm, aortic dissection, aortic regurgitation, mitral regurgitation and aortic dissection which usually occurs in previously normal sized aorta are poor prognostic factors. However, the aortic dissection which developed in patient with Marfan syndrome and aortic aneurysm was rare. We experienced one case of dissecting aneurysm in patient diagnosed as previous aortic aneurysm, aortic regurgitation, and Marfan syndrome, receiving successful operation.
