Frontal-orbital internal distraction for severe proptosis in school-aged Crouzon syndrome
10.3760/cma.j.cn114453-20211018-00409
- VernacularTitle:额眶内牵张成骨术治疗突眼严重的学龄期Crouzon综合征
- Author:
Jie CUI
1
;
Weimin SHEN
;
Yi JI
;
Liangliang KONG
;
Jianbing CHEN
Author Information
1. 南京医科大学附属儿童医院烧伤整形外科，南京 210008
- Keywords:
Craniosynostoses;
Craniofacial abnormalities;
Osteogenesis, distraction;
Crouzon syndrome;
Proptosis
- From:
Chinese Journal of Plastic Surgery
2022;38(12):1358-1363
- CountryChina
- Language:Chinese
-
Abstract:
Objective:To investigate the effect of intrafrontal-orbital distraction osteogenesis in the treatment for school-aged children with severe proptosis in Crouzon syndrome.Methods:We retrospectively analyzed the clinical data of school-aged children with Crouzon syndrome treated with intrafrontal orbital distraction osteotomy at the Children’s Hospital of Nanjing Medical University from January 2016 to February 2021, and counted and analyzed the clinical results, complications (cerebrospinal fluid leakage, infection, etc.), and surgical safety.Results:A total of 12 children, 9 males and 3 females, aged 6-12.1 years, with an average age of 7.1 years, were included; 4 were cranial, 6 were craniofacial, and 2 were other types. All were shown with obvious proptosis. The surgical procedure was successful. Follow-up ranged from 3 to 20 months, with a mean of 14 months. The postoperative distraction distance was (19.1±3.3) mm, ranging from 15.2 to 25.6 mm. And the mean cranial index (CI) before and after surgery were 97.5% and 80.0%, respectively, with good craniofacial appearance and better improvement of proptosis and posterior cranial flattening. There were no other complications but for one child with infection at the external site of the distraction rod.Conclusions:The effect of frontal-orbital distraction osteotomy in the treatment of Crouzon syndrome with severe proptosis in school-aged children was positive, with significant improvement in proptosis and low incidence of postoperative cerebrospinal fluid leakage and infection. This procedure is a good choice for older children with severe proptosis.
