Anesthetic Management of a Patient with Tuberous Sclerosis Undergoing Bilateral Nephrectomy: A case report.
10.4097/kjae.2006.50.2.228
- Author:
Dongchul LEE
1
;
Kyung Cheon LEE
;
Hong Sun KIM
;
Hyun Jeong KWAK
;
Ki Tae MOON
Author Information
1. Department of Anesthesiology and Pain Medicine, Gacheon Medical School Gil Medical Center, Incheon, Korea. hyun615@hanmail.net
- Publication Type:Case Report
- Keywords:
anesthesia;
nephrectomy;
tuberous sclerosis
- MeSH:
Adolescent;
Anesthesia;
Angiofibroma;
Blood Gas Analysis;
Female;
Humans;
Intellectual Disability;
Kidney;
Nephrectomy*;
Seizures;
Thiopental;
Tuberous Sclerosis*;
Vital Signs
- From:Korean Journal of Anesthesiology
2006;50(2):228-231
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Tuberous sclerosis is an autosomal dominantly transmitted genetic disorder that has characteristic symptoms triad of mental retardation, convulsion, and facial angiofibroma. Because it is a relatively uncommon disorder, there are few informations about anesthetic management for this disorder. We report a case of tuberous sclerosis that had involved bilateral kidneys. A 14-year old female patient was induced with thiopental sodium, rocuronium bromide and then intubated with an internal diameter 6.5 mm of reinforced tube. Anesthesia was maintained with O2-N2O-isoflurane. Surgery took 3 hours and there were no remarkable changes in vital signs and arterial blood gas analysis.
