Malignant Peripheral Nerve Sheath Tumor of Abdomen.
- Author:
Kyu Sub SO
1
;
Yeung Kook LIM
;
Yong Taek HONG
;
Hoon Nam KIM
Author Information
1. Department of Plastic and Reconstructive Surgery, Fatima Hospital, Daegu, Korea. psdrlyk@yahoo.co.kr
- Publication Type:Case Report
- Keywords:
Malignant peripheral nerve sheath tumor;
Abdomen mass
- MeSH:
Abdomen;
Aged, 80 and over;
Biopsy;
Hemorrhage;
Humans;
Neurofibromatosis 1;
Peripheral Nerves;
Recurrence;
Skin;
Ulcer
- From:Journal of the Korean Society of Plastic and Reconstructive Surgeons
2011;38(6):886-889
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
PURPOSE: Malignant peripheral nerve sheath tumor without neurofibromatosis type 1 is very rare neoplasm. Development in the superficial soft tissue is exremely rare. Authors experienced one rare case of primary malignant peripheral nerve sheath tumor developed on abdomen. The clinical and histologic findings were described. METHODS: An 83-year-old man visited hospital with an 11x6.5x4.5 cm sized ulcerated and hemorrhagic mass on abdomen. The tumor was localized in abdominal skin and started growing 3 years ago. RESULTS: Wide excision with safety margin of 2cm and limberg flap was done. The postoperative biopsy revealed a malignant peripheral nerve sheath tumor. There was no evidence of recurrence of tumor for 16 months. CONCLUSION: Malignant peripheral nerve sheath tumor is an aggressive malignant tumor. An abrupt enlargement of size, ulceration and bleeding are suggestive of malignant chnages of the tumor. We recommand early wide excision with enough safety margin as treatment of malignant peripheral nerve sheath tumor.
