Coexistence of the Renal Fibromuscular Dysplasia and Familial Adenomatous Polyposis.
- Author:
Jeong Min CHA
1
;
Kang Won LEE
;
Jae Hoon LEE
;
Yu Min LEE
;
Sung Won JUNG
;
Ji Eun LEE
;
Jin Ho SHIN
;
Ju Hung SONG
;
Hun Su KIM
;
Hyang Jung CHO
;
Seon Ho AHN
Author Information
1. Department of Internal Medicine, Wonkwang University School of Medicine, Iksan, Korea. yumin0525@hanmail.net
- Publication Type:Case Report
- Keywords:
Fibromuscular dysplasia (FMD);
Familial adenomatous polyposis (FAP);
Renovascular hypertension
- MeSH:
Adenomatous Polyposis Coli*;
Angioplasty;
Carotid Artery, Internal;
Colectomy;
Colorectal Neoplasms;
Female;
Fibromuscular Dysplasia*;
Humans;
Hypertension;
Hypertension, Renovascular;
Polyps;
Renal Artery;
Tomography, X-Ray Computed;
Vascular Diseases;
Young Adult
- From:Korean Journal of Nephrology
2007;26(6):779-783
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disease that most commonly affects the renal and internal carotid arteries. A Familial adenomatous polyposis (FAP) is characterized by hundreds of adenomatous colorectal polyps, with an almost inevitable progression to colorectal cancer. A 19-year-old woman with history of total colectomy as a result of familial adenomatous polyposis presented with high blood pressure incidentally. Abdominal CT scan showed "string of beads" appearance of right renal artery. Percutaneous transluminal renal angioplasty was performed and then hypertension was improved. To our knowledge, there has been no previous case report of secondary renovascular hypertension resulting from fibromuscular dysplasia in patients with FAP. Here, we report a patient with a review of the literature.
