Ganglioneuroblastoma with WDHA Syndrome.
- Author:
Dae Yeon KIM
1
;
Ki Hong KIM
;
Sang Beom KIM
;
Sung Eun JUNG
;
Seong Cheol LEE
;
Kwi Won PARK
;
Woo Ki KIM
Author Information
1. Department of Surgery, Seoul National University College of Medicine, Seoul, Korea.
- Publication Type:Original Article
- Keywords:
WDHA syndrome;
Ganglioneuroblastoma;
VIP
- MeSH:
Achlorhydria;
Adrenal Glands;
Diarrhea;
Drug Therapy;
Female;
Ganglioneuroblastoma*;
Humans;
Hypokalemia;
Infant;
Vipoma*
- From:Journal of the Korean Association of Pediatric Surgeons
2000;6(1):56-59
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The syndrome of watery diarrhea, hypokalemia, and achlorhydria (WDHA syndrome) is rare, and occasionally related with neurogenic tumors. A 20-month-old girl presenting symptoms of WDHA syndrome was transferred to our hospital. She had a ganglioneuroblastoma of adrenal gland. The serum level of VIP was elevated. After complete excision of tumor, all symptoms of WDHA syndrome were improved. The postoperative course was uneventful, and symptoms of WDHA syndrome disappeared. The serum level of VIP dropped to normal. The girl with postoperative chemotherapy and radiation therapy survived without evidence of disease for 33 months after complete resection.
