Anesthetic Management of a Patient with Alexander's Disease: Case Report.
10.12701/yujm.2010.27.1.47
- Author:
Bum Soo KIM
1
;
Dae Lim JEE
;
Sun Ok SONG
Author Information
1. Department of Anesthesiology, College of Medicine, Yeungnam University, Daegu, Korea. adjee@med.yu.ac.kr
- Publication Type:Case Report
- Keywords:
Alexander's disease;
Leukodystrophy;
Anesthesia;
Seizure
- MeSH:
Adolescent;
Alexander Disease;
Anesthesia;
Brain;
European Continental Ancestry Group;
Femur;
Humans;
Male;
Muscle Spasticity;
Perioperative Period;
Seizures
- From:Yeungnam University Journal of Medicine
2010;27(1):47-51
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We present here the case of a 13-year-old male patient with Alexander's disease who underwent surgical correction of a femur fracture. Alexander's disease is a rare and fatal disorder that affects the white matter in the brain and it causes developmental delay, psychomotor regression, spasticity, megaloencephaly and seizure. The patient had the possibility of a seizure attack during the perioperative period. We discuss the anesthetic management of a patient with Alexander's disease and we review the relevant literature.
