A Case of Adult Onset Still's Disease Presented with Acute Febrile Hepatitis.
- Author:
Sang Jun LEE
1
;
Hong Sung CHOUGH
;
Min Keun CHO
;
Jee Sun NA
;
Hyun Sook KIM
;
Man Woo KIM
Author Information
1. Department of Internal Medicine, Chosun University College of Medicine, Gwangju, Korea. healthyra@chosun.ac.kr
- Publication Type:Case Report
- Keywords:
Hepatitis;
Adult-onset Still's disease
- MeSH:
Adult;
Arthritis;
Cardiac Tamponade;
Disseminated Intravascular Coagulation;
Early Diagnosis;
Exanthema;
Fever;
Hepatitis;
Humans;
Leukocytosis;
Liver Diseases;
Liver Failure;
Lymphatic Diseases;
Lymphohistiocytosis, Hemophagocytic;
Pharyngitis;
Respiratory Distress Syndrome, Adult;
Splenomegaly;
Still's Disease, Adult-Onset
- From:Korean Journal of Medicine
2011;80(5):620-624
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Adult-onset Still's Disease (AOSD) is a rare, immune-mediated, multisystem inflammatory disorder characterized by quotidian spiking fevers, an evanescent rash, arthritis, lymphadenopathy, splenomegaly, a sore throat, leukocytosis, and liver dysfunction. Its clinical manifestations are very diverse, from relatively mild symptoms to severe complications, such as disseminated intravascular coagulation, cardiac tamponade, acute respiratory distress syndrome, hemophagocytic syndrome, and hepatic failure. Hepatic failure is an extremely rare complication that could lead to death. Therefore, early diagnosis and treatment are important. We report a case of adult-onset Still's disease with acute febrile hepatitis.