Periumbilical Perforating Pseudoxanthoma Elasticum in a Young Male Patient.
- Author:
Sang Woo LEE
1
;
Ji Yeon BYUN
;
You Won CHOI
;
Ki Bum MYUNG
;
Hae Young CHOI
Author Information
1. Department of Dermatology, School of Medicine, Ewha Womans University, Seoul, Korea. hychoi@ewha.ac.kr
- Publication Type:Case Report
- Keywords:
Periumbilical perforating pseudoxanthoma elasticum;
Young man
- MeSH:
Adult;
Angioid Streaks;
Biopsy;
Connective Tissue;
Elastic Tissue;
Female;
Humans;
Hypertension;
Male;
Middle Aged;
Obesity;
Pregnancy;
Pseudoxanthoma Elasticum;
Risk Factors;
Skin
- From:Korean Journal of Dermatology
2011;49(12):1135-1137
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Periumbilical perforating pseudoxanthoma elasticum is a rare acquired disorder of connective tissue. It has been suggested that repeated traumas of pregnancy, obesity, or abdominal surgery promote localized degeneration of elastic fibers. Most cases reported in the English literature occurred in obese, middle aged, multiparous women. We describe a 29-year-old male who had two hyperpigmented plaques on the periumbilical area. He had angioid streaks, but was not obese and did not have hypertension. A skin biopsy revealed transepidermal elimination of degenerated and calcified elastic fibers, which was consistent with periumbilical perforating pseudoxanthoma elasticum. We report an interesting case of periumbilical perforating pseudoxanthoma elasticum that occurred in a young man with no known predisposing risk factors.
