A Case of Epidermolysis Bullosa Dystrophica.
- Author:
Song OH
;
Sung Choon LIM
;
Eul Nam HAN
;
Nack In KIM
;
Choong Rim HAW
- Publication Type:Case Report
- Keywords:
EBD ( Epidermolysis bullosa dystriphica )
- MeSH:
Blister;
Child, Preschool;
Cicatrix;
Epidermolysis Bullosa Dystrophica*;
Epidermolysis Bullosa*;
Female;
Fingers;
Foot;
Humans;
Parturition;
Skin;
Syndactyly;
Toes
- From:Korean Journal of Dermatology
1985;23(3):387-391
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Epidermolysis bullosa dystrophica(EBD) is a rare, hereditary and chronic mechanobullous disease characterized by blistering and erosions of the skin in response to even minor trauma. A 5-year old girl visited with a complaint of continuous vesicobullous skin eruptions since birth. On examination, bullae, vesicles, atrophic scars, crusts and ero:ions were scattered on whole body. Loss of finger and toe nails, partial syndactyly of all toe webs and milia on dorsa of feet were noticed. We present a case of EBD that seems to be a recessive type considering the absence of family history with histopathologic and electron microscopic findings.