Acquired C1 inhibitor deficiency associated with SLE.
- Author:
Ea Wha KANG
1
;
Jang Yel SHIN
;
Dong Ryeal RYU
;
Jungsik SONG
;
Won Ki LEE
;
Yong Beom PARK
;
Soo Kon LEE
Author Information
1. Division of Rheumatology, Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
- Publication Type:Original Article
- Keywords:
Lupus erythematosus, Systemic;
Angioneurotic edema;
Acquired C1 inhibitor deficiency
- MeSH:
Adult;
Angioedema;
Angioedemas, Hereditary*;
Female;
Humans;
Lupus Erythematosus, Systemic
- From:Korean Journal of Medicine
2001;61(1):91-94
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Acquired C1 inhibitor deficiency is a rare syndrome which usually presents with episodes of angioedema. The association of lupus erythematosus and angioneurotic edema has been previously reported but is usually related to hereditary C1 inhibitor deficiency. Currently the relationship between acquired C1 inhibior deficiency and lupus erythematosus is being discussed. So we report the case of a previously healthy 28-year-old woman, who developed simultaneously and acquired angioneurotic edema and systemic lupus erythematosus.