A Case of Phakomatosis Pigmentovascularis Type I a With Multiple Pyogenic Granulomas Developed in Pregnancy.
- Author:
Yong Joo MOON
1
;
Soo Jung JANG
;
Yong Ho CHOI
;
Jee Youn WON
;
Gi Dong JUNG
Author Information
1. Department of Dermatology, Presbyterian Medical Center, Chonju, Korea. dallmoon@yahoo.co.kr
- Publication Type:Case Report
- Keywords:
Phakomatosis pigmentovascularis;
Ppyogenic granuloma
- MeSH:
Adult;
Female;
Granuloma, Pyogenic*;
Humans;
Neurocutaneous Syndromes*;
Nevus;
Port-Wine Stain;
Pregnancy*
- From:Korean Journal of Dermatology
2003;41(9):1210-1214
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Phakomatosis pigmentovascularis(PPV) was first described in 1947 as a distinctive association of vascular and pigmentary nevi by Ota et al. Hasegawa et al subclassified the disorder into eight types and type I a is characterized by the coexistence of nevus flammeus and nevus pigmentosus et verrucous, which is not associated with systemic organ involvement. PPV type I a is relatively rare and a case with multiple pyogenic granulomas developed in pregnancy, is not reported yet. We present a case of PPV type I a with multiple pyogenic granulomas developed in pregnancy within nevus flammeus in a 29-year-old female.
