A case of arrhythmogenic right ventricular cardiomyopathy/dysplasia involving the left ventricle.
- Author:
Young Keun KIM
1
;
Jeong Hee KIM
;
Dong Gyu KIM
;
Kyoung Tae JEONG
;
Yu Jeong CHOI
;
Sahng LEE
;
Soon Chang PARK
Author Information
1. Department of Internal Medicine, Eulji University Hospital, Daejeon, Korea. jhkim999@eulji.ac.kr
- Publication Type:Case Report
- Keywords:
Arrhythmogenic right ventricular cardiomyopathy;
Left ventricle
- MeSH:
Arrhythmogenic Right Ventricular Dysplasia;
Bundle-Branch Block;
Cardiopulmonary Resuscitation;
Death, Sudden, Cardiac;
Defibrillators;
Echocardiography;
Electrocardiography;
Heart Ventricles;
Humans;
Magnetic Resonance Imaging;
Military Personnel;
Myocardium;
Tachycardia, Ventricular;
Ventricular Fibrillation;
Ventricular Premature Complexes;
Young Adult
- From:Korean Journal of Medicine
2009;76(Suppl 1):S64-S69
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Arrhythmogenic right ventricular cardiomyopathy (ARVC)/dysplasia is characterized by fibro-fatty replacement of the right ventricular myocardium. A 19-year-old soldier was admitted with sudden cardiac arrest that presented as ventricular fibrillation requiring cardiopulmonary resuscitation. His electrocardiogram (ECG) showed normal sinus rhythm with inverted T waves from leads V1 to V4 and isolated premature ventricular beats with a left bundle branch block (LBBB) pattern. Echocardiography showed that the right ventricle was enlarged with apical trabecular formation. The coronary angiogram was normal. Cardiovascular magnetic resonance imaging (MRI) showed thinning and fatty substitution of both the right and left ventricular free walls. Ventricular tachycardia (LBBB pattern) occurred frequently despite anti-arrhythmic drug treatment. His drug-resistant ventricular tachycardia was treated with an implanted cardiac defibrillator. Left ventricle involvement in ARVC is less common and more severe. Cardiac MRI is considered the best imaging technique for evaluating the right ventricle and diagnosing ARVC.
