Time is Gut. Approaching Intestinal Leiomyositis: Case Presentation and Literature Review
10.5223/pghn.2024.27.4.197
- Author:
Michail AFTZOGLOU
1
;
Christina HEINRICH
;
Till Sebastian CLAUDITZ
;
Thomas MENTER
;
Deborah DORTH
;
Konrad REINSHAGEN
;
Ingo KÖNIGS
Author Information
1. Department of Pediatric Surgery, Altona Children’s Hospital, Hamburg, Germany
- Publication Type:Review Article
- From:Pediatric Gastroenterology, Hepatology & Nutrition
2024;27(4):197-205
- CountryRepublic of Korea
- Language:English
-
Abstract:
T-lymphocytic intestinal leiomyositis is a rare cause of “pediatric intestinal pseudoobstructions.” Diagnosis may be difficult and requires full-thickness bowel biopsies during laparotomy or laparoscopy with possible enterostomy. Currently, immunosuppressive therapy is the only available treatment. A delay in diagnosis and therapy may negatively affect the prognosis because of ongoing fibrotic alterations; therefore, early diagnosis and consequent treatment are crucial. This review summarizes the available information on the nosology, diagnostic steps, and treatment modalities. Here, we report the youngest case of enteric leiomyositis reported in the last two decades and analyze its management by reviewing previous cases.
