Bullous Congenital Ichthyosiform Erythroderma: Report of a Case.
- Author:
Doo Chan MOON
;
Kyung Sool KWON
;
Tae An CHUNG
- Publication Type:Case Report
- MeSH:
Blister;
Extremities;
Female;
Humans;
Hyperkeratosis, Epidermolytic*;
Skin;
Vacuoles
- From:Korean Journal of Dermatology
1981;19(4):445-501
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We present a case of bullous congenital ichthyosiform erythroderma in a two year old female, in whom no hereditary background was found. The skin lesion was characterized clinically by blister formation with generalized erythematous hyperkeratosis which was especially prominent on the flexural surfaces of extremities and intertriginous areas. The histopathologic examination revealed marked hyperkeratosis, cavity changes of the malpighian cells with perinuclear vacuoles and markedly thickened granular layer containing many keratohyaline granules.
