Partial agenesis of dorsal pancreas with Castleman's disease in pancreatic tail area.
- Author:
Sooyoung PARK
1
;
Seungmin BANG
;
Myoung Hwan KIM
;
Han Jak RYU
;
Jae Bock CHUNG
;
Woo Jung LEE
;
Si Young SONG
Author Information
1. Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea. sysong@yumc.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Castleman's disease;
Agenesis;
Pancreas
- MeSH:
Cholangiopancreatography, Endoscopic Retrograde;
Embryonic Development;
Female;
Giant Lymph Node Hyperplasia*;
Humans;
Magnetic Resonance Imaging;
Mediastinum;
Middle Aged;
Pancreas*;
Pancreatic Ducts;
Pregnancy
- From:Korean Journal of Medicine
2006;71(1):80-85
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Agenesis of dorsal pancreas is a very rare congenital anomaly which comes from the failure of development of the body and tail of pancreas in embryogenesis. Castleman's disease is a rare lymphoid tumor which usually occurred in the mediastinum, but it is very uncommon in the retroperitoneal pancreatic tail area. We report a case of partial agenesis of dorsal pancreas with Castleman's disease in pancreatic tail area, mimicking a pancreatic tumor. A 46-year-old woman was admitted to our hospital with intermittent abdominal discomfort for 2 months. Computed tomography, magnetic resonance imaging, and endoscopic retrograde cholangiopancreatography (ERCP) revealed a tumor at distal pancreatic tail area, short pancreatic duct, and absence of pancreatic body and tail. The surgical excision of the tumor revealed hyaline-vascular type Castleman's disease.