A Case of Berry Syndrome associated with Syndactyly.
- Author:
Sang Chun JUNG
1
;
Kyoung Sim KIM
;
Yong Wook KIM
;
Ki Bok KIM
Author Information
1. Department of Pediatrics, Kwangju Christian Hospital, Kwangju, Korea.
- Publication Type:Case Report
- Keywords:
Berry syndrome;
Syndactyly;
Two-dimensional echocardiography
- MeSH:
Aorta, Thoracic;
Diagnosis;
Echocardiography;
Fruit*;
Heart;
Humans;
Intracranial Hemorrhages;
Male;
Palate;
Prognosis;
Pulmonary Artery;
Syndactyly*
- From:Journal of the Korean Pediatric Society
1998;41(4):543-547
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Berry syndrome is a rare association of congenital heart anomalies which consists of a distal aortopulmonary window with aortic origin of the right pulmonary artery and hypoplasia or interruption of the aortic arch. This defect can be corrected only by immediate surgical intervention, so accurate preoperative diagnosis and detailed anatomic depiction of this syndrome are important in prognosis. We experienced a case of Berry syndrome in an 8-day-old male, who had presented with multiple malformation such as syndactyly, high arched palate and brain hemorrhage. The diagnosis was made by two-dimensional echocardiography. The case is presented with a brief review of related literatures.
