Recommendations for the diagnosis and treatment of IgG 4-related disease in China
10.3760/cma.j.cn112138-20221105-00830
- VernacularTitle:IgG 4相关性疾病诊疗规范
- Author:
Yunyun FEI
1
;
Yanying LIU
;
Lingli DONG
;
Yang XIANG
;
Wen ZHANG
;
Yan ZHAO
Author Information
1. 中国医学科学院 北京协和医学院 北京协和医院风湿免疫科 国家皮肤与免疫疾病临床医学研究中心 疑难重症和罕见病国家重点实验室 风湿免疫病教育部重点实验室，北京 100730
- Keywords:
IgG 4-related disease;
Diagnosis;
Treatment;
Evaluation;
Prognosis
- From:
Chinese Journal of Internal Medicine
2023;62(10):1161-1171
- CountryChina
- Language:Chinese
-
Abstract:
IgG 4-related disease (IgG 4-RD) is an immune-mediated fibroinflammatory condition characterized by tumefactive lesions in multi-organs. It is a novel entity presented by variable manifestations. In recent years, there has been progress toward recognizing IgG 4-RD. However, the diagnosis and treatment of IgG 4-RD still present challenges due to insufficient experience. To address this, the Chinese Rheumatology Association has developed standardized guidelines for the diagnosis and treatment of IgG 4-RD based on domestic and international experience. These guidelines aim to enhance the understanding and management of IgG 4-RD, ultimately improving the prognosis for patients with IgG 4-RD.
