Perioperative nursing care of a child with erythropoietic protoporphyria undergoing liver transplantation and splenectom
10.3761/j.Issn.0254-1769.2023.23.014
- VernacularTitle:1例红细胞生成性原卟啉病患儿行肝移植及脾切除的围手术期护理
- Author:
Fang WANG
1
;
Fangyan LU
;
Yan WANG
Author Information
1. 310003 杭州市 浙江大学医学院附属第一医院肝移植中心
- Keywords:
Erythropoietic Protoporphyria;
Liver Transplantation;
Splenectomy;
Perioperative Nursing;
Pediatric Nursing
- From:
Chinese Journal of Nursing
2023;58(23):2915-2919
- CountryChina
- Language:Chinese
-
Abstract:
To summarize the perioperative nursing experience of a child with erythropoietic protoporphyria who underwent liver transplantation and splenectomy.The key points of preoperative care include implementing diversified interventions to reduce the accumulation of porphyrin in the body;actively controlling pain and improving the comfort of children;early debridement and treatment,and good care of solar allergic dermatitis.The key points of postoperative care include protecting the transplanted liver and preventing the deposition of protoporphyrin;strengthening respiratory management to control lung infection;psychological counseling throughout the process to reduce negative emotions;individualized follow-up management to prepare for bone marrow transplantation.After careful treatment and nursing,the child recovered smoothly and was discharged from the hospital.A follow-up visit after 1 month discharge showed a good recovery.
