A Case of Lupus Nephritis Associated with Transiently Decreased C1 Inactivator Activity and Angioedema.
- Author:
Su Jin OH
1
;
yung Pyo KANG
;
Yong Bum JANG
;
Sang Woo NAM
;
Myung Jae KANG
;
Sik LEE
;
Sung Kwang PARK
;
Sung Kyew KANG
;
Won KIM
Author Information
1. Department of Internal Medicine, Chonbuk National University Medical School, Korea. kwon@chonbuk.ac.kr
- Publication Type:Case Report
- Keywords:
Lupus erythematosus;
Systemic;
Nephritic;
Angioedema;
Acquired C1 esterase deficiency
- MeSH:
Angioedema*;
Angioedemas, Hereditary;
Autoimmune Diseases;
Female;
Humans;
Lupus Erythematosus, Systemic;
Lupus Nephritis*;
Lymphoproliferative Disorders;
Young Adult
- From:Korean Journal of Nephrology
2005;24(5):828-831
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
C1 esterase inhibitor deficiency with consequent angioedma is an uncommon condition. Nonhereditary C1 inhibitor deficiency includes underlying disorders; lymphoproliferative disorder, autoimmune disease, hypereosinophilia, drug-induced, allergic, and idiopathic forms. The as sociation of hereditary C1 esterase inhibitor deficiency with systemic lupus erythematosus has been previously described. We experienced a case with transiently decreased C1 inactivator activity and angioedema in lupus nephritis. This present case is a previously healthy 22-year-old woman, who developed intermittent facial angioedema and decreased urine amount. After steroid treatment, the C1 inactivator activity was recovered and angioedema was disappeared.
