A Clinical Study of 30 Cases of Pityriasis Rubra Pilaris.
- Author:
Kyung Sook KWON
1
;
Kyung Hyung SEO
;
Ho Sun JANG
;
Tae Ahn CHUNG
Author Information
1. Department of Dermatology, College of Medicine, Pusan National University, Pusan, Korea.
- Publication Type:Original Article
- Keywords:
Clinical study;
Griffiths' classification;
Pityriasis rubra pilaris
- MeSH:
Classification;
Foot;
Humans;
Incidence;
Pityriasis Rubra Pilaris*;
Pityriasis*;
Prognosis;
Rare Diseases;
Retrospective Studies
- From:Korean Journal of Dermatology
1996;34(6):924-932
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
BACKGROUND: Pityriasis rubra pilaris (PRP) is a rare disease characterized by widespread follicular acuminate papules. Traditionally, two forms have been described : hereditary (juvenile) and acquired (generally aduIrt). A.substantial contribution, however, suggests that further subdivision is appropriate. OBJECTIVE: The purpose of this study was to investigate clinicopathologic features of PRP and to compare the results of clinical classification with Griffiths' classification. METHODS: The retrospective clinicopathologic study carried out in 30 cases of PRP over the last 30 years. RESULTS: 1. The incidence of type lV was 38.5%. For both type I and III it was 30.8%. The onset ages of the type I, III, and lV were 36.1, 6.0, and 96 years respectively. 2. The most common site of initial involvement was the palms, and the most common involvement site during the diease course was the dorsa of palms and feet. The incidence involved in the whole body was 46.6%. 3. The incidences of insidious and acute onset were 60% and 40% respectively. No case had the family history of PRP. 4. In the histopathologic study, diffuse hyperkeratosis, acanthosis, and mild dermal infiltrations were found in all cases. Follicular pluggings were observed in 93.3% of cases CONCLUSION: We investigated the clinical classifications and clinicopathologic features of PRP. We think that more studies such as prognosis and treatment of PRP should be achieved in the near future.
