A Case of Juvenile Xanthogranuloma Developed in a Neurofibromatosis Child with Family History.
- Author:
Hyun Deok SEO
1
;
Ji Young SONG
;
Byoung Soo CHUNG
;
Kyu Cherl CHOI
;
Bong Seok SHIN
Author Information
1. Department of Dermatology, Chosun University Medical School, Gwangju, Korea. Derm75@hanmail.net
- Publication Type:Case Report
- Keywords:
Juvenile chronic myelogenous leukemia;
Juvenile xanthogranuloma;
Neurofibromatosis
- MeSH:
Child;
Humans;
Infant;
Leukemia, Myelomonocytic, Juvenile;
Neurofibromatoses;
Risk Factors;
Skin;
Xanthogranuloma, Juvenile
- From:Korean Journal of Dermatology
2008;46(4):547-549
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Juvenile xanthogranuloma (JXG) is a fibrohistiocytic proliferative disorder predominant in infancy and childhood. It is a benign and transient skin lesion that usually appears in the cephalic area. Recently, the concurrent finding of neurofibromatosis (NF), juvenile chronic myelogenous leukemia (JCML), and JXG has been repeatedly reported. Especially, the family history of NF may represent a risk factor for the development of JCML in patients with NF and in patients with NF and JXG. So, a finding of JXG and NF in infants should alert the physician to a possible development of JCML. We report a case of JXG developed in a neurofibromatosis child with family history.
