Analysis of Surgical Treatment of 20 Cases of Ebstein's Anomaly Combined with Atrial Septal Defect
10.12259/j.issn.2095-610X.S20240115
- VernacularTitle:三尖瓣下移畸形合并房间隔缺损20例手术治疗结果分析
- Author:
Xiong JIN
1
;
Runwei MA
;
Chunjie MU
Author Information
1. 云南省阜外心血管病医院心外科,云南 昆明 650102
- Keywords:
Ebstein's anomaly;
Atrial septal defect;
Surgery correction;
Atrial Septal fenestration;
Therapeutic outcomes
- From:
Journal of Kunming Medical University
2024;45(1):87-92
- CountryChina
- Language:Chinese
-
Abstract:
Objective To analyze the treatment strategy of the atrial septal defect in the surgical treatment of Ebstein's anomaly combined with the atrial septal defect and the short-term follow-up results of the treatment of Ebstein's anomaly.Methods A retrospective analysis of the clinical data and follow-up results of 20 patients with Ebstein's anomaly and atrial septal defect was conducted from September 2017 to February 2021.And the statistical analysis on the preoperative and postoperative echocardiography results of this group of patients was performed.Results Sixteen patients underwent the biventricular correction surgery,among whom two cases underwent the horizontal atrial tricuspid valvuloplasty(Danielsons procedure),four cases underwent the vertical atrial tricuspid valvuloplasty(Carpentier procedure),and ten cases underwent the conical reconstruction.Two patients were given a half ventricular correction surgery(tricuspid valve reconstruction combined with bidirectional Glenn surgery)and two patients underwent the bidirectional Glenn surgery.The combined atrial septal defects were closed in one stage during extracorporeal circulation for correction of deformitie in 20 patients.At 1,3,6,and 12 months after the surgery,the patient's right ventricular size significantly decreased compared to preoperative(P<0.05),and cardiac function(left ventricular ejection fraction)significantly improved(P<0.05).Conclusion The surgical treatment of Ebstein's anomaly combined with the atrial septal defect should follow the principle of individualized treatment.Biventricular correction is still the first choice for the treatment of Ebstein's anomaly,and the atrial septal defect should be closed at one stage,so as to obtain a good therapeutic effect.
