A Case of Intraductal Papillary Mucinous Neoplasm Arising from Santorini's Duct in a Patient with Complete Type of Pancreas Divisum.
10.4166/kjg.2009.54.5.337
- Author:
Mi Jin KIM
1
;
Ju Sang PARK
;
Jun Hyung CHO
;
Chi Woon CHA
;
Yun Jung OH
Author Information
1. Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea. parkjs@dmc.or.kr
- Publication Type:Case Report ; English Abstract
- Keywords:
Intraductal papillary mucinous neoplasm;
Santorini's duct;
Pancreas divisum
- MeSH:
Adenocarcinoma, Mucinous/*diagnosis/etiology;
Aged;
Carcinoma, Pancreatic Ductal/*diagnosis/etiology;
Carcinoma, Papillary/*diagnosis/etiology;
Cholangiopancreatography, Endoscopic Retrograde;
Cholangiopancreatography, Magnetic Resonance;
Diagnosis, Differential;
Female;
Humans;
Pancreatic Ducts/abnormalities/*surgery;
Pancreatic Neoplasms/*diagnosis/etiology
- From:The Korean Journal of Gastroenterology
2009;54(5):337-341
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
There have been an increasing number of reports of intraductal papillary mucinous neoplasms (IPMNs) of the pancreas since its first report by Ohhasi et al. in 1982. Most IPMNs arise from Wirsung's duct or its branches, whereas IPMNs arising from Santorini's duct are rare. Pancreas divisum is a common congenital anatomical anomaly characterized by the lack of fusion of the ventral and dorsal parts of the pancreas during the eighth week of fetal development. Although clinical significance of pancreas divisum has been the subject of debate for many years, there seems to be little doubt that in certain patients there is a causal relation between pancreas divisum and pancreatitis. Also, it is occasionally accompanied by a pancreatic tumor. Herein, we report a case of IPMN arising from Santorini's duct in patient with complete type of pancreas divisum.