Imaging Findings of Arteriovenous Malformations Involving Lung and Liver in Hereditary Hemorrhagic Telangiectasia (Osler-Weber- Rendu Disease): Two Cases Report.
10.3348/jkrs.1999.41.3.503
- Author:
Jeong Geun YI
1
;
Joo Hyuk LEE
;
Su Ok SEONG
Author Information
1. Department of Radiology, Cheongju St. Mary's Hospital, Korea.
- Publication Type:Case Report
- Keywords:
Arteriovenous malformations, hepatic;
Arteriovenous malformations, pulmonary;
Telangiectasia
- MeSH:
Angiography;
Arteries;
Arteriovenous Malformations*;
Brain;
Gastrointestinal Tract;
Hemorrhage;
Hepatic Artery;
Hepatic Veins;
Liver*;
Lung*;
Radiography;
Telangiectasia, Hereditary Hemorrhagic*;
Telangiectasis;
Thorax;
Tomography, Spiral Computed;
Veins
- From:Journal of the Korean Radiological Society
1999;41(3):503-506
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Hereditary hemorrhagic telangiectasia (HHT) or Osler-Weber-Rendu disease is an autosomal dominant disorder characterized by repeated episodes of bleeding. Multiple telangiectases consisting of thin-walled, dilated vascular channels with arteriovenous communication may involve, for example, mucocutaneous tissue, the gastrointestinal tract, and the liver, lung, and brain. We report the imaging findings of two cases of HHT involving arteriovenous malformation of both the lungs and liver, a rare condition. Chest radiography revealed a round mass, while helical CT showed a feeding artery and draining vein with arteriovenous malformation in the lung. Color Doppler sonography revealed an enlarged and tortuous hepatic artery with high systolic velocity. CT demonstrated an enlarged hepatic artery, arteriovenous shunt, and early draining hepatic vein in the liver. Celiac angiography showed arteriovenous malformation.
