Intravenous Leiomyomatosis with Extension to the Heart Associated with Disseminated Peritoneal Leiomyomatosis.
10.3904/kjm.2016.91.2.185
- Author:
Young Lee JUNG
1
;
Rak Kyeong CHOI
;
Moon Yong EOM
;
Hyun A CHO
;
Woong CHOI
;
Dong Jin KIM
;
Ui Geun HAM
Author Information
1. Division of Cardiology, Department of Internal Medicine, Sejong General Hospital, Bucheon, Korea. Yoorimbin@sejongh.co.kr
- Publication Type:Case Report
- Keywords:
Leiomyomatosis;
Desseminated peritoneal leiomyomatosis;
Intravenous leiomyomatosis
- MeSH:
Adult;
Cardiopulmonary Bypass;
Female;
Heart*;
Humans;
Laparotomy;
Leiomyoma;
Leiomyomatosis*;
Myocytes, Smooth Muscle;
Peritoneum;
Sternotomy;
Vena Cava, Inferior
- From:Korean Journal of Medicine
2016;91(2):185-190
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Leiomyomatosis refers to benign smooth muscle cell tumors that often arise from unusual growth patterns and include benign metastasizing leiomyoma, disseminated peritoneal leiomyomatosis, and intravenous leiomyomatosis. Intravenous leiomyomatosis is the extension of a vascular tumor into the venous channels, whereas disseminated peritoneal leiomyomatosis is characterized by multiple leiomyomas growing along the submesothelial tissues of the abdominopelvic peritoneum. It is extremely rare for intravenous leiomyomatosis and disseminated peritoneal leiomyomatosis to occur simultaneously. A 42-year-old female presented with disseminated peritoneal leiomyomatosis and intravenous leiomyomatosis extended through the inferior vena cava into the right side of the heart. The patient underwent one-stage surgery under simultaneous sternotomy and laparotomy, and radical excision of the tumor was achieved using cardiopulmonary bypass. Here we describe a case in which complete removal of a leiomyomatosis with an unusual growth pattern was successfully performed using one-stage surgery.
