A Case of Adrenogenital Syndrome.
- Author:
Heung Shik OH
1
Author Information
1. Department of Urology, School of Medicine, Chonnam National University, Korea.
- Publication Type:Case Report
- Keywords:
adrenogenital syndrome
- MeSH:
Adolescent;
Adrenal Glands;
Adrenal Hyperplasia, Congenital;
Adrenogenital Syndrome*;
Androgens;
Circumcision, Female;
Clitoris;
Female;
Genitalia;
Heterosexuality;
Humans;
Male;
Metabolism;
Penis;
Perineum;
Urethra
- From:Korean Journal of Urology
1973;14(3):239-244
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The adrenogenital syndrome owing to congenital adrenal hyperplasia is an inborn error of adreno-cortical metabolism, as a result of excessive adrenal androgens. producing heterosexual virlizing changes in females and isosexual precocity in males. Here, a case of adrenogenital syndrome developed in 14 year-old Korean female was presented. She had an enlarged clitoris and vaginal introitus communicated to the urethra interior to the urethral meatal opening at the perineum, resembling perineal hypospadiac penis. Exploration of the pelvic cavity and left adrenal gland revealed normal female internal genital organs and hyperplastic adrenal gland. Constructive operation including vaginoplasty and clitoridectomy was performed.