Anesthetic management of children with Beckwith-Wiedemann syndrome : Two cases report.
10.4097/kjae.2009.56.5.583
- Author:
Hyun Joo KIM
1
;
Jin Tae KIM
;
Hyun Jung KIM
;
Hee Soo KIM
;
Chong Sung KIM
;
Seong Deok KIM
Author Information
1. Department of Anesthesiology and Pain Medicine, Seoul National University College of Medicine, Seoul, Korea. kimjintae73@dreamwiz.com
- Publication Type:Case Report
- Keywords:
Anesthesia;
Beckwith-Wiedemann syndrome;
Glossectomy;
Hypoglycemia;
Macroglossia
- MeSH:
Anesthesia;
Beckwith-Wiedemann Syndrome;
Child;
Glossectomy;
Heart Diseases;
Hernia, Umbilical;
Humans;
Hypoglycemia;
Macroglossia
- From:Korean Journal of Anesthesiology
2009;56(5):583-586
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Beckwith-Wiedemann syndrome consists of various abnormalities, including macroglossia, visceromegaly, omphalocele, and neonatal hypoglycemia. These abnormalities frequently require operative correction and careful anesthetic management. Principal problems associated with anesthetic management in this syndrome are congenital heart disease, hypoglycemia, and difficult airway combined with macroglossia. We report two cases of general anesthetic management in children with Beckwith-Wiedemann syndrome.
