A Case of Hemophilia B with Abdominal and Pelvic Pseudotumor
10.12376/j.issn.2097-0501.2022.04.016
- VernacularTitle:血友病B伴腹盆腔假肿瘤一例
- Author:
Jing ZHANG
1
,
2
,
3
;
Mankai JU
1
,
2
,
3
;
Kemin ZHANG
2
,
3
,
4
;
Lingling CHEN
1
,
2
,
3
;
Yuhua WANG
2
,
3
,
5
;
Lei ZHANG
1
,
2
,
3
;
Renchi YANG
1
,
2
,
3
;
Feng XUE
1
,
2
,
3
Author Information
1. Thrombosis and Hemostasis Center, National Clinical Research Center for Blood Diseases, State Key Laboratory of Experimental Hematology, National Hemophilia Registry Center, Institute of Hematology &
2. Blood Diseases Hospital, Chinese Academy of Medical Sciences &
3. Peking Union Medical College, Tianjin 300020, China.
4. Department of Imaging, National Clinical Research Center for Blood Diseases, State Key Laboratory of Experimental Hematology, National Hemophilia Registry Center, Institute of Hematology &
5. Coagulation Laboratory, National Clinical Research Center for Blood Diseases, State Key Laboratory of Experimental Hematology, National Hemophilia Registry Center, Institute of Hematology &
- Publication Type:Journal Article
- Keywords:
hemophilia B;
pseudotumor;
imaging manifestations
- From:
JOURNAL OF RARE DISEASES
2022;1(4):456-460
- CountryChina
- Language:Chinese
-
Abstract:
Hemophilia B is a genetic disorder caused by coagulation factor Ⅸ(FⅨ) deficiency, mainly manifesting as joint, muscle and deep tissue bleeding. Hemophilia pseudotumor is a mass formed by soft tissue liquefaction and necrosis caused by repeated bleeding. Most pseudotumors occur in the bone and muscle. We report a case of hemophilia B with pseudotumor formation in the pelvis and abdomen, where lesion location is relatively rare. After active and effective hemostasis, the patient's hematuria symptom gradually improved. This case suggests that early and timely hemostatic treatment is crucial for patients with hemophilia.
