A Case Report of Gorham-Stout Syndrome with Kyphoscoliosis
10.12376/j.issn.2097-0501.2023.04.016
- VernacularTitle:Gorham-Stout综合征合并脊柱侧后凸一例
- Author:
Chenkai LI
1
,
2
;
Shengru WANG
1
,
2
;
Ziquan LI
1
,
2
;
Nan WU
1
,
2
,
3
;
Jianguo ZHANG
1
,
2
,
3
Author Information
1. Department of Orthopaedic Surgery, Beijing Key Laboratory for Genetic Research of Skeletal Deformity, Key Laboratory of Big Data for Spinal Deformities, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences &
2. Peking Union Medical College, Beijing 100730, China.
3. Peking Union Medical College, Beijing 100730, China.State Key Laboratory of Complex Severe and Rare Diseases, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences &
- Publication Type:Journal Article
- Keywords:
Gorham-Stout syndrome;
kyphoscoliosis;
chylothorax
- From:
JOURNAL OF RARE DISEASES
2023;2(4):602-606
- CountryChina
- Language:Chinese
-
Abstract:
This article reported the treatment of Gorham Stout syndrome (GSS) with kyphoscoliosis. The patient was an 11-year-old male who was presented with kyphoscoliosis, first developed 4 years ago, accompanied by incomplete paralysis of both lower limbs. The syndrome worsened in the previous year. He had a history of chylothorax, ventilation dysfunction, and osteoporosis. The patient underwent skull traction in another hospital for 7 months, which was ineffective. Finally, he underwent posterior correction, internal fixation, and bone graft fusion (C4-T8) in our hospital. The postoperative clinical outcomes and the posterior correction were satisfactory, with significant improvement in incomplete paralysis of both lower limbs. This article aims to improve the understanding of GSS and provided reference for its diagnosis and treatment through a typical case report and review of previous literature.
