Surgical Treatment of Ebstein Anomaly.
- Author:
Jong Ho LEE
1
;
Byung Yul KIM
Author Information
1. Department of Thoracic and Cardiovascular surgery, National Medical Center.
- Publication Type:Original Article
- Keywords:
Ebstein anomaly
- MeSH:
Atrial Septum;
Atrioventricular Block;
Congenital Abnormalities;
Ebstein Anomaly*;
Follow-Up Studies;
Foramen Ovale;
Heart Ventricles;
Humans;
Pulmonary Valve Stenosis;
Sex Distribution;
Sex Ratio;
Survivors;
Tachycardia, Sinus;
Tricuspid Valve;
Tricuspid Valve Insufficiency
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
1999;32(1):5-9
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
BACKGROUND: Ebstein anomaly is a rare congenital disease distinguished by its unique deformity in tricuspid valve and right ventricle & atrium. In its surgical treatment , tricuspid valve reconstruction and valve replacement are well known method, but various surgical methods were suggested. MATERIAL AND METHOD: From January 1984 to December 1995, 8 patients with Ebstein anomaly underwent surgical correction. Age and sex distribution, clinical symtoms, radiologic findings, preoperative studies, operative findings, operative methods and its results were analyzed. RESULT: The sex ratio was 5 to 3(male : female). Patients' ages were averaged 17.6(2-28) years. In all cases, it showed typical deformities of the tricuspid valve. Associated anomalies were permenant foramen ovale, atrial septum defect, pulmonary stenosis. Surgical procedures included tricuspid valve replacement(n=4) and tricuspid valve reconstuction(n=4). Two cases of sinus tachycardia and complete AV block occured postoperatively. There were two hospital death and no late death. All survivors are in NYHA class I or II with median follow up of 64.8 months. 2-D echocardiogram disclosed improvement tricuspid regurgitation during the follow up period. CONCLUSION: Even though operative method of Ebstein anomaly should be decided according to each anatomical characteristics, we recommended that tricuspid valvuloplasty and plication can be one of the good methods method in the selective cases.
